Cystic Fibrosis: References

  1. Cystic Fibrosis Foundation Patient Registry 2006 Annual Data Report to the Center Directors. © 2007 Cystic Fibrosis Foundation, Bethesda, MD.

  2. Quinton, P. M. 1999. Physiological basis of cystic fibrosis: a historical perspective. Physiol Rev 79(1 Suppl):S3-S22. PubMed

  3. Rock, M. J. 2007. Newborn screening for cystic fibrosis. Clin Chest Med 28(2):297-305. PubMed

  4. 2005. ACOG Committee Opinion. Number 325, December 2005. Update on carrier screening for cystic fibrosis. Obstet Gynecol 106(6):1465-8. PubMed

  5. Rosenstein, B. J., and G. R. Cutting. 1998. The diagnosis of cystic fibrosis: A consensus statement. J Pediatr 132(4):589-595. PubMed

  6. Robinson, T. E. 2007. Imaging of the chest in cystic fibrosis. Clin Chest Med 28(2):405-21. PubMed

  7. Cystic Fibrosis Foundation Clinical Practice Guidelines for Cystic Fibrosis Treatment of Pulmonary Exacerbation of Cystic Fibrosis 1997. Cystic Fibrosis Foundation, Bethesda, MD.

  8. Moran, A., D. Hardin, D. Rodman, H. F. Allen, R. J. Beall, D. Borowitz, C. Brunzell, P. W. Campbell, 3rd, S. E. Chesrown, C. Duchow, R. J. Fink, S. C. Fitzsimmons, N. Hamilton, I. Hirsch, M. S. Howenstine, D. J. Klein, Z. Madhun, P. B. Pencharz, A. L. Quittner, M. K. Robbins, T. Schindler, K. Schissel, S. J. Schwarzenberg, V. A. Stallings, W. B. Zipf, and et al. 1999. Diagnosis, screening and management of cystic fibrosis related diabetes mellitus: a consensus conference report. Diabetes Res Clin Pract 45(1):61-73. PubMed

  9. Yankaskas, J. R., B. C. Marshall, B. Sufian, R. H. Simon, and D. Rodman. 2004. Cystic fibrosis adult care: consensus conference report. Chest 125(1 Suppl):1S-39S. PubMed

  10. Sueblinvong, V., and L. A. Whittaker. 2007. Fertility and pregnancy: common concerns of the aging cystic fibrosis population. Clin Chest Med 28(2):433-43. PubMed

  11. Hardin, D. S., J. Rice, R. C. Cohen, K. J. Ellis, and J. A. Nick. 2005. The Metabolic Effects of Pregnancy in Cystic Fibrosis. Obstet Gynecol 106(2):367-375. PubMed

  12. Tonelli, M. R., and M. L. Aitken. 2007. Pregnancy in cystic fibrosis. Curr Opin Pulm Med 13(6):537-40. PubMed

  13. Rodman, D. M., J. M. Polis, S. L. Heltshe, M. K. Sontag, C. Chacon, R. V. Rodman, S. J. Brayshaw, G. A. Huitt, M. D. Iseman, M. T. Saavedra, L. M. Taussig, J. S. Wagener, F. J. Accurso, and J. A. Nick. 2005. Late Diagnosis Defines a Unique Population of Long-term Survivors of Cystic Fibrosis. Am J Respir Crit Care Med 171(6):621-6. PubMed

  14. Flume, P. A., B. P. O'Sullivan, K. A. Robinson, C. H. Goss, P. J. Mogayzel, Jr., D. B. Willey-Courand, J. Bujan, J. Finder, M. Lester, L. Quittell, R. Rosenblatt, R. L. Vender, L. Hazle, K. Sabadosa, and B. Marshall. 2007. Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med 176(10):957-69. PubMed

  15. Elkins, M. R., and P. T. Bye. 2006. Inhaled hypertonic saline as a therapy for cystic fibrosis. Curr Opin Pulm Med 12(6):445-52. PubMed

  16. Ramsey, B. W., H. L. Dorkin, J. D. Eisenberg, R. L. Gibson, I. R. Harwood, R. M. Kravitz, D. V. Schidlow, R. W. Wilmott, S. J. Astley, and M. A. McBurnie. 1993. Efficacy of aerosolized tobramycin in patients with cystic fibrosis. N Engl J Med 328(24):1740-6. PubMed

  17. Liou, T. G., F. R. Adler, D. R. Cox, and B. C. Cahill. 2007. Lung transplantation and survival in children with cystic fibrosis. N Engl J Med 357(21):2143-52. PubMed

  18. Sueblinvong, V., B. T. Suratt, and D. J. Weiss. 2007. Novel therapies for the treatment of cystic fibrosis: new developments in gene and stem cell therapy. Clin Chest Med 28(2):361-79. PubMed

  19. Dorfman R, Sandford A, Taylor C, Huang B, Frangolias D, Wang Y, Sang R, Pereira L, Sun L, Berthiaume Y, Tsui LC, Paré PD, Durie P, Corey M, and J. Zielenski. 2008. Complex two-gene modulation of lung disease severity in children with cystic fibrosis. J Clin Invest. 2008 Mar;118(3):1040-9. PubMed

Clinical Trials

Impact of Combination Therapy on Cystic Fibrosis (TEACH Study)

The purpose of this study is to determine how two medications, azithromycin and inhaled tobramycin, work when taken together to treat cystic fibrosis (CF) patients with chronic pseudomonas aeruginosa (PA) lung infections.

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